Bernard-Soulier syndrome

Bernard Soulier syndrome (BSS) is an inherited platelet disorder characterized by mild to severe bleeding tendency, macrothrombocytopenia and absent ristocetin-induced platelet agglutination.

Also known as: Hemorrhagiparous thrombocytic dystrophy, giant platelet disorder, isolated, giant platelet syndrome, BSS, Platelet glycoprotein 1b, deficiency of, deficiency of platelet glycoprotein 1b

Category: General

What is Bernard-Soulier syndrome?

Bernard-Soulier syndrome is a recognized medical condition. This page explains what it is, symptoms that may accompany it, and the lab tests healthcare providers sometimes use to investigate it. It is educational information only and is not a diagnosis.

If you think you may have Bernard-Soulier syndrome, speak with a qualified healthcare provider for evaluation and guidance.

Symptoms that may be associated with Bernard-Soulier syndrome

Abnormal bleedingBruising susceptibilityEpistaxisGastrointestinal hemorrhageGingival bleedingHematemesisMenorrhagiaMigraineProlonged bleeding after dental extractionProlonged bleeding after surgeryProlonged bleeding timeSeizure

When to seek medical care

Seek medical advice if you have symptoms that are severe, persistent, or affecting your daily life. Emergency care is needed for symptoms like chest pain, difficulty breathing, confusion, or severe weakness.